肺原发性韦格纳肉芽肿1例:附文献综述

A Case Report and Literature Review of Pulmonary Wegener’Granulomatosis

韦格纳肉芽肿(Wegener’granulomatosis,WG)是一种病情发展迅速的自身免疫性疾病,可累及肺、肾脏等全身各个器官,未得到早期诊疗的患者死亡率较高。由于WG发病率极低且缺乏特异性影像学特征,常导致临床漏诊、误诊和治疗延误。本文报道1例55岁女性患者,因肺部结节经皮肺穿刺活检确诊为肺原发性WG的诊疗经过,并对相关文献进行了综述。

Wegener’granulomatosis is an autoimmune diseases,often involving the lung and kidney,has a high mortality rate in nontreatment patients.The low incidence and nonspecific features,often lead to misdiagnosis and delayed treatment.This paper reported the diagnosis and treatment of a 55-year-old female patient with primary Wegener’granuloma of the lung diagnosed by percutaneous lung biopsy of pulmonary nodules,and reviews the relevant literature.