上皮样血管内皮瘤MRI表现

MRI manifestations of epithelioid hemangioendothelioma

目的观察上皮样血管内皮瘤(EHE)MRI表现。方法回顾性分析经病理证实的23例EHE患者,均接受病灶部位MR平扫,其中21例接受增强MR扫描,观察其MRI表现。结果23例中,骨EHE 8例,肝脏EHE 8例,皮肤或肌肉软组织EHE 3例,颅内EHE 2例,鼻腔、心血管EHE各1例;15例为单发病灶,8例见多发(3~36个)病灶。平扫T1WI中,20例病灶呈低信号、2例呈等信号、1例呈混杂信号;T2WI中,18例呈混杂信号、3例呈高信号、2例呈等信号。22例接受弥散加权成像检查,其中20例病灶呈高信号、2例呈等信号。21例接受增强扫描,12例病灶明显不均匀强化、9例轻度不均匀强化。结论EHE的MRI表现具有一定特征性,结合临床有助于诊断。

Objective To observe MRI manifestations of epithelioid hemangioendothelioma(EHE).Methods Data of 23 patients with EHE confirmed by pathology were retrospectively analyzed.Among them,23 patients underwent plain and 21 underwent enhanced MR scanning of the lesions site,and the MRI manifestations were observed.Results There were 8 cases of bone EHE,8 of liver EHE,3 of skin or muscle soft tissue EHE,2 of intracranial EHE,1 of nasal cavity EHE and 1 of cardiovascular EHE,15 cases with single lesion and 8 cases with multiple(3-36)lesions in each case.Plain MR T1WI showed low signals in 20 cases,isosignals in 2 cases and mixed signals in 1 case,while T2WI showed heterogeneous intensities in 18 cases,high signals in 3 cases and isointensities in 2 cases.Totally 22 patients underwent diffusion weighted imaging,hyperintensities were observed in 20 cases and isointensities in 2 cases.Among 21 patients who underwent enhanced MR scanning,obviously heterogeneous enhancement was found in 12 cases while mildly heterogeneous enhancement was noticed in 9 cases.Conclusion MRI manifestations of EHE had certain characteristics,which were helpful to diagnosis combining with clinical findings.