骨纤维结构不良伴动脉瘤样骨囊肿1例报告

One case report of osteofibrous dysplasia with aneurysmal bone cyst

骨纤维结构不良属于骨良性肿瘤性病变,以骨纤维变性为特征。动脉瘤样骨囊肿因局限性病损,且外周有骨膜反应骨沉积,类似于动脉瘤样膨胀而得名,但两者结合较少见。动脉瘤样骨囊肿因其发病率低,临床易误诊。目前病理学检查为其诊断的主要手段,影像学检查可为其在确诊前提供较高的诊断依据,手术为其主要的治疗方法。笔者收集陕西中医药大学附属医院2021年9月诊治为骨纤维结构不良伴动脉瘤样骨囊肿并采用股骨病灶刮除及取髂骨植骨手术治疗的患者1例,通过查阅相关文献,对这一少见疾病的影像学、病理学、临床诊断及治疗进行讨论。

Osteofibrous dysplasia is a benign neoplastic lesion characterized by bone fibrodegeneration.Aneurysmal bone cysts get their name because of localized lesions and periperiosteal reactive bone deposits similar to aneurysmal distension,but the combination of the two is rare.Due to its low incidence,it is easy to be misdiagnosed.At present,pathological examination is the main means of diagnosis,imaging examination can provide a higher diagnosis basis before diagnosis,and surgery is the main treatment.Author collected one patient diagnosed with osteofibrous dysplasia with aneurysmal bone cyst and treated with femoral lesion curettage and iliac bone grafting in the Affiliated Hospital of Shaanxi University of Chinese Medicine in September 2021,and discussed the imaging,pathology,clinical diagnosis,and treatment of this rare disease by reviewing relevant literature.