节段型皮肤僵硬综合征一例

Segmental stiff skin syndrome: a case report

我们报道一例节段型皮肤僵硬综合征。患者,男,14岁。腹部皮肤硬化6年。病理活检示:真皮深层胶原纤维增生,成纤维细胞增多,散在的脂肪细胞灶,浅筋膜胶原纤维粗大,阿新蓝染色阴性。

We report a case of segmental stiff skin syndrome.A 14-year-old man attended our clinic with a 6-year history of the skin induration on his abdomen.Histological examination revealed broadened and elongated collagen fibrils in deep dermis,increased fibrocytes,clusters of lipocytes,thickening collagen fibrils in superficial fascia,alcian blue staining was negative.