胎儿期腹膜后原始神经外胚层肿瘤一例

A case of retroperitoneal primitive neuroectodermal tumor in fetus

PNET是一种较为罕见的高度恶性的神经系统肿瘤,分为周围型和中枢型两种类型。位于腹膜后的PNET更为罕见。PNET发病机制及病因目前尚不明确。由于PNET本身较少见,对于胎儿期发现的PNET的生物学特性与临床转归尚缺乏系统研究,临床报道很少。其确诊依靠病理检查,胎儿期PNET极易误诊。本文报道一例胎儿期腹膜后原始神经外胚层肿瘤病例。

PNET is a rare and highly malignant tumor of the nervous system, which can be divided into two types:peripheral and central. Retroperitoneal PNETs are more rare. The pathogenesis and etiology of PNET are still unclear. Because PNET itself is rare, there is still a lack of systematic research on the biological characteristics and clinical outcomes of PNETs found in the fetus, and there are few clinical reports. The diagnosis depends on pathological examination, and PNET in fetus is easily misdiagnosed. This article reports a case of a retroperitoneal primitive neuroectodermal tumor in the fetus.