残角子宫伴右肾缺如一例并文献复习

Rudimentary Uterus Horn with Absense of Right Kidney: A Case Report and Literature Review

苗勒管畸形是女性生殖道的先天性畸形,残角子宫(rudimentary uterus horn)就是由于其中一条苗勒管发育受阻形成的。该畸形通常在青春期得以明确诊断,而在青春期之前常因无明显症状而漏诊。该畸形的初始临床症状并无特异性,患者可表现为痛经、不孕、慢性或急性腹痛等症状。报告1例23岁有8年痛经史的患者,最终诊断为残角子宫伴右肾缺如,回顾性分析其分型、诊断及治疗资料,旨在提醒临床上对年轻腹痛患者宜将苗勒管异常作为一个重要的鉴别诊断。

Müllerian duct anomalies are congenital malformations of the female genital tract,the rudimentary uterus horn is the result of blocked development of one of the Müllerian tubes.These abnormalities are usually diagnosed during puberty,because they tend to remain asymptomatic until adolescence.The initial clinical symptoms are nonspecific and may include dysmenorrhea,infertility,and chronic or acute abdominal pain.A 23-year-old patient with 8-year history of dysmenorrhea was reported.The final diagnosis was Rudimentary uterus horn with absense of right kidney.By discussing its typing,diagnosis and treatment,it is intended to remind clinicians that Müllerian anomalies should always be considered as an important differential diagnosis in young patients with abdominal pain.