摘要
Dear editor,Vulvar sarcomas are rare and represent 1%–3%of cancers in this region.1 Leiomyosarcoma is the most common type of vulvar sarcoma.In contrast,epithelioid sarcoma(ES)is extremely rare,accounting for around 1%of soft-tissue vulvar sarcomas.Among the ESs of the vulva,proximal variants tend to have a more aggressive clinical course,in comparison to distal variants.2 The treatment of choice in proximal-type ES of the vulva is surgical resection,usually with surgical margins greater than 2 cm.Due to the extreme rarity of these malignancies,clear algorithms for adjuvant treatment of these tumors have still not been established.Radiotherapy and/or chemotherapy may be indicated in some cases.
