先天性孤立肾单中心病例总结

Single-center experience of congenital solitary kidney cases

目的探讨先天性孤立肾(CSK)患者病情特点。方法收集了2012-2020年北京协和医院诊断为先天性孤立肾的患者,对其病例资料及术后随访结果进行分析。结果共纳入本院233例CSK患者,男性58例,女性175例。其中最常见伴发畸形为生殖道畸形,其次为先天性脊柱侧凸。15%的CSK患者存在其他肾脏相关疾病。5例患者行泌尿外科手术,随访中均未出现术后并发症。仅1例肾部分切除术后1年出现复发转移,遂行二次手术治疗。结论发现CSK畸形的同时,有必要进行全身多系统的评估。此类患者即使症状隐匿也应定期监测,就诊治疗过程更需谨慎保护肾功能。

Objective To summarize the characteristics of patients with congenital solitary kidney(CSK).Methods Medical data and post-operative follow up results of patients that was diagnosed with congenital solitary kidney in Peking Union Medical College Hospital from 2012 to 2020 were collected.Results A total of 233 patients with congenital solitary kidney(58 males and 175 females)were included in this study.The most common deformity was genital tract deformity followed by congenital scoliosis.15%of CSK patients had other renal disease.Urological surgery was performed in 5 patients,and no postoperative complications occurred during follow-up.Only 1 patient presented recurrence and metastasis 1 year after partial nephrectomy and underwent secondary surgery.Conclusions When congenital solitary renal malformation is screened out,it is necessary to carry out systemic evaluation.As for surgical treatment,it should be carefully executed,and long-term follow-up should be conducted to monitor renal function.