黏多糖贮积症Ⅵ型合并妊娠患者的围手术期护理

Perioperative nursing of a pregnancy patient withⅥmucopolysaccharidoses

总结1例黏多糖贮积症Ⅵ型合并妊娠患者围手术期的护理体会。护理要点:针对该患者情绪焦虑、担忧胎儿结局,身材矮小、脊柱发育异常、舌大,胸廓小、肋间肌膈肌等运动受损,肌力下降、活动受限及心功能Ⅱ级的问题,采取术前心理支持性护理、舒适度改善性指导、活动安全性管理、心力衰竭动态性防护、母儿多学科监测措施;术后采取体液精确性平衡、气道严密性监护、并发症周密性防控及母婴亲密性构建措施。经过精心诊疗护理,患者于剖宫产术后第6天出院;新生儿于出生后第43天从新生儿科出院,母儿结局良好。

To summarize the perioperative nursing experience of a pregnancy patient with Ⅵ mucopolysaccharidoses. In view of the problems of emotional anxiety,worry about fetal outcome,short stature,abnormal spine development,large tongue,small thoracic size,intercostal diaphragm impaired movements,limited muscle strength and cardiac function grade Ⅱ in this patient,key points of nursing included preoperative psychological supportive care,comfort improvement guidance,activity safety management,heart failure dynamic protection,maternal and fetal multidisciplinary monitoring,postoperative fluid precision balance,close airway monitoring,complication prevention,maternal and infant intimacy building measures. After careful treatment and nursing,the patient was discharged on the sixth day after cesarean section. The newborn was discharged from the Neonatal Department on the 43rd day after birth. Both of the maternal and fetal outcome were well.