孕期肝门区囊肿:囊肿型胆道闭锁与胆总管囊肿的鉴别

Hepatic hilar cyst during pregnancy:differential diagnosis of cystic biliary atresia and choledochal cyst

胆道闭锁(biliary atresia,BA)是新生儿期常见梗阻性黄疸的病因。按梗阻的部位及程度分为3型,其中Ⅰ型囊肿型胆道闭锁(cystic biliary atresia,CBA)是少见但又特殊的一种亚型,其在临床表现、影像学检查等方面都与先天性胆总管囊肿(choledochal cyst,CC)有着相似的表现,两者也是产前诊断最常发现的肝门区囊性病变,但因两者的治疗方案及预后有着显著的差异,因此,迄今为止两者的鉴别仍然是临床医生需要破解的难题,本文将对目前已有的相关研究成果进行综述。

Biliary atresia(BA)is a common cause of obstructive jaundice due to cholestasis during neonatal period.According to the location and degree of obstruction,cystic biliary atresia(CBA)type I is a rare and yet special subtype.It has similar clinical manifestations and imaging findings to those of congenital choledochal cyst(CC).Cystic changes are detected prenatally in hepatic portal area.However,significant differences exist in treatments and prognoses of two diseases.So far,a proper differentiation has remained a perplexing problem for clinicians.This review summarized the latest researches of the differential diagnosis.