艾森曼格综合征合并妊娠剖宫产后脓毒症死亡1例报道

Eisenmenger syndrome complicated with sepsis after cesarean section:a death case report

妊娠合并心脏病是导致孕产妇死亡的非产科病因之一,发病率为0.5%~3.0%。合并艾森曼格综合征的孕产妇死亡率高达30%~50%,最终剖宫产者高达65%~75%。妊娠合并重度肺动脉高压属于妊娠禁忌证,临床能够足月妊娠者较少见,一旦确诊需尽早终止妊娠。本文报道1例妊娠32+3周合并艾森曼格综合征患者的诊治过程,进一步分析救治失败的原因,以提高医生对本病的认识及重视程度,尽早开展多学科管理,进而提高救治成功率。

Pregnancy complicated with heart disease is one of the non-obstetric causes of maternal death,with an incidence rate of 0.5%-3.0%.The maternal mortality rate with Eisenmenger syndrome is as high as 30%-50%,and the final cesarean section rate is as high as 65%-75%.Pregnancy complicated with severe pulmonary hypertension is a contraindication of pregnancy,and full-term pregnancy is rare.Once diagnosed,it is necessary to terminate the pregnancy as soon as possible.This paper reported the diagnosis and treatment process of a 32+3 week gestation patient with Eisenmenger syndrome and pulmonary hypertension,and further analyzed the causes of treatment failure,in order to improve doctors’awareness and attention to this disease,to carry out multidisciplinary management as soon as possible,and to improve the success rate of treatment.