盆腔IgG4相关性腹膜后纤维化误诊一例

IgG4-Related Retroperitoneal Fibrosis of the Pelvis:A Case Report

本文报道了盆腔IgG4相关性腹膜后纤维化误诊为淋巴瘤1例。患者女,44岁,因B超体检发现双侧附件包块2月余入院,既往曾行双侧下颌包块切除术,病理不详。胸部CT平扫提示纵隔内及双侧腋窝多发肿大淋巴结。盆腔MRI表现为盆腔腹膜后间隙多发大小不等软组织肿块影,T_(2)WI呈等/稍低信号,脂肪抑制T_(2)WI信号较子宫肌层信号稍低,T_(1)WI呈等信号,增强扫描动脉期呈中等强化,静脉期及延迟期强呈明显均匀强化,病灶沿髂血管旁和盆腔后壁分布,未见大血管被包绕。行腹腔镜下取材手术,病理证实为IgG4相关性腹膜后纤维化。

This paper reports a case of pelvic IgG4-related retroperitoneal fibrosis misdiagnosed as lymphoma.A 44-year-old female patient was admitted to the hospital due to the discovery of bilateral adnexal masses during physical examination for more than 2 months.She had previously undergone bilateral mandibular mass excision.The pathology is unknown.Chest CT showed multiple lymphadenopathy in the mediastinum and bilateral axilla.Pelvic MRI showed multiple soft tissue masses of different sizes in the retroperitoneal space of the pelvis,with iso/hypointense on T_(2)WI and isointense on T_(1)WI,moderate enhancement in arterial phase,and further enhancement in venous phase and delayed phase.The posterior wall of the pelvis was distributed,and no large blood vessels were found to be surrounded.After laparoscopic surgery,the pathological diagnosis was IgG4-related retroperitoneal fibrosis.