骨肥大静脉曲张综合征合并假性Kaposi肉瘤1例

Klippel-Trenaunay-Weber Syndrome with Pseudo Kaposi's Sarcoma:A Case Report

患者女,45岁,跛行40年,左下肢斑块35年,加重1年。查体见左下肢长、粗于右下肢。皮肤科情况:左足背、左足内踝及小腿处可见暗紫至暗褐色斑块,局部少量白色鳞屑,局部结痂,无压痛,左足皮损皮温明显高于右足。皮损组织病理符合假性Kaposi肉瘤。诊断:骨肥大静脉曲张综合征合并假性Kaposi肉瘤。给予患者口服阿维A、雷公藤多苷、复方甘草酸苷片,外用多磺酸黏多糖乳膏,嘱患者避免久站及日常穿戴弹力袜等局部加压治疗。

A 45-year-old female presented with limping for 40 years and left lower extremity plaque for 35 years,aggravated for one year.Physical examination showed that the left lower extremity was longer and thicker than the right lower extremity.Dermatological conditions:dark purple to dark brown plaques were seen on the left dorsum,left medial malleolus and calf,with a small amount of white scales locally,local crusting,and no tenderness.The skin temperature of the left foot was significantly higher than that of the right foot.The histopathology of the skin lesions was consistent with pseudo-Kaposi's sarcoma.The diagnosis of Klippel-Trenaunay-Weber syndrome with pseudo Kaposi's sarcoma was made.The patients were given oral acitretin,tripterygium glycosides,compound glycyrrhizin tablets,and topical polysulfonic acid mucopolysaccharide cream.The patients were instructed to avoid prolonged standing and daily wear of elastic stockings and other local compression treatments.