先天性喉裂诊疗专家共识

Consensus recommendations on the evaluation and treatment of congenital laryngeal clefts

先天性喉裂是一个罕见的气道畸形,主要表现为呛咳、喂养困难等,影响患儿的生长发育;严重的喉裂可以表现为严重的呛咳误吸,导致阵发性青紫,甚至死亡。随着内镜技术的发展,使得喉裂可以被早期发现和诊断。不同类型的喉裂治疗方案差异较大,早期的诊断与评估对于儿童耳鼻喉科医生至关重要。中国医师协会儿科医师分会儿童耳鼻咽喉专业委员会联合全国多家儿童医疗中心讨论拟定诊治共识,从症状学、客观检查等方面给出喉裂的诊断治疗方案,为临床规范化诊疗提供指导性意见。

Congenital laryngeal cleft is a rare airway malformation,mainly manifested as choking,feeding difficulties,which affects the growth and development of children.Patients with a severe laryngeal cleft may have recurrent aspiration,leading to cyanotic spells,or even death.Advances in development of endoscopic techniques have made early diagnosis possible.Depending on the degree of cleft,management may involve a variety of approaches ranging from medical management alone to open repair.Therefore,it is important for pediatric ENT doctors to diagnose and evaluate in clinical practice.This consensus statement,developed by the Pediatric otorhinolaryngology Professional Committee of the Pediatrician Branch of the Chinese Medical Doctor Association,provides comprehensive recommendations and standardized guidance on diagnosis and management of laryngeal cleft,based on symptomatology,physical examinations,and laboratory tests.