项部巨大肌上皮肿瘤1例并文献复习

Giant myoepithelial carcinoma of the nuchal region:a case report and literature review

肌上皮肿瘤,又称恶性肌上皮瘤,是一种罕见的起源于肌上皮细胞的恶性肿瘤。本文报道1例伴巨大项部肿物、左肘部肿物的患者,在局部麻醉下行超声引导项部及肘部肿物穿刺,病理诊断为肌上皮肿瘤。在全身麻醉下,切除下颈部、后颅窝、颈部和左肘的巨大肿瘤,术后病理显示均为肌上皮肿瘤。免疫组织化学显示AE1/AE3(+)、P63(+)、CK7(+)、CK5(+),CD138(+)。现对本病例的临床特征和诊治经过进行报告及相关文献复习。

Myoepithelioma,also known as malignant myoepithelioma,is a rare malignant tumor originating from myoepithelial cell.This article reports a patient with a huge tumor in the neck and left elbow who underwent fine needle aspiration under local anesthesia.The pathological diagnosis was a myoepithelioma.Under general anesthesia,giant tumors in the lower neck,posterior cranial fossa,neck,and left elbow were removed,and postoperative pathology showed that they were all myoepithelial tumors.Immunohistochemistry showed AE1/AE3(+),P63(+),CK7(+),CK5(+),and CD138(+).The clinical characteristics and diagnosis and treatment process of this case are reported and relevant literature is reviewed.