二维超声心动图联合时间-空间复合成像对胎儿Berry综合征的诊断价值

Diagnostic value of two-dimensional echocardiography combined with spatio-temporal image correlation in fetal Berry syndrome

目的 总结胎儿Berry综合征的二维超声心动图和时间-空间复合成像(STIC)图像特征,探讨其临床价值。方法 回顾性分析8例产前超声诊断为Berry综合征胎儿的二维超声心动图、彩色多普勒超声及STIC图像资料,总结胎儿Berry综合征的超声心动图表现。结果 8例Berry综合征胎儿均表现为主-肺动脉间隔缺损(Ⅰ型3例、Ⅱ型5例)、主动脉弓离断(A型6例、B型2例)及右肺动脉起源于升主动脉;3例为孤立性Berry综合征,5例合并其他心内结构异常(2例合并永存左上腔静脉,2例合并右位主动脉弓并迷走左锁骨下动脉,1例合并右室双出口)。8例患儿的STIC图像均清晰显示了主动脉弓离断位置及左、右肺动脉起源。结论 二维超声心动图联合STIC可准确诊断胎儿Berry综合征,具有重要的临床价值。

Objective To summarize the characteristics of two-dimensional echocardiography and spatio-temporal image correlation(STIC)of fetal Berry syndrome,and to explore its clinical value.Methods The two-dimensional echocardiography,color Doppler ultrasound and STIC data of 8 fetal Berry syndrome diagnosed by prenatal ultrasound were retrospectively analyzed,and the echocardiographic manifestations of Berry syndrome were summarized.Results All the 8 fetal Berry syndrome were showed aortopulmonary septal defect(3 cases of typeⅠand 5 cases of typeⅡ),interruption of aortic arch(6 cases of type A and 2 cases of type B),abnoraml origin of right pulmonary from asendibg artery.3 cases were isolated Berry syndrome and 5 cases were complicated with other intracardiac structural malformations(2 cases with persistent left superior vena cava,2 cases with right aortic arch and aberrant left subclavian artery,and 1 case with double outlet of right ventricle).The STIC images of 8 fetal Berry syndrome clearly showed the amputated location of aortic arch and the origin of left and right pulmonary arteries.Conclusion Two-dimensional echocardiography combined with STIC can accurately diagnose fetal Berry syndrome,which has important clinical value.