胚胎发育不良性神经上皮肿瘤影像学表现

Imaging Features of Dysembryoplastic Neuroepithelial Tumors

目的:掌握胚胎发育不良性神经上皮肿瘤(DNET)的影像学表现,提高对本病的诊断能力。方法:回顾性分析病理证实的36例DNET临床及影像学资料,评估其临床及影像学特征。结果:36例患者男女比例为22∶14,发病率20岁以下为50%,30岁以下比例达80.56%;所有病例均为单发,58.3%位于颞叶,25%位于额叶;MRI表现为T1WI低信号,T2WI高信号;T2-FLAIR失配征28例,增强扫描5例病灶壁结节强化;MRI分型:Ⅰ型类囊性24例,Ⅱ型结节状5例,Ⅲ型发育异常样7例。结论:DNET的影像学表现具有一定的影像学特征性,磁共振对DNET术前分型具有重要帮助。

Purpose:To evaluate the imaging features of dysembryoplastic neuroepithelial tumor(DNET)and improve the diagnosis of this disease.Methods:The data of 36 cases of DNETs confirmed by pathology results were analyzed retrospectively,and their clinical and imaging characteristics were evaluated.Results:The ratio of male and female in 36 patients was 22:14.Of all the patients,50%were under the age of 20,and 80.56%were under 30 years old.All cases were with single lesion,58.3%located in the temporal lobe and 25%in the frontal lobe.MRI showed low intensity signal on TIWI and high intensity signal on T2WI.There were 28 cases with T2-FLAIR mismatch sign and 5 cases of focal wall nodule enhancement on the enhanced scan.MRI classification:type I(cystic)in 24 cases,type II(nodular)in 5 cases,and type II(dysplasia)in 7 cases.Conclusion:The imaging manifestations of DNET are with certain imaging characteristics,and MRI is of great help to the preoperative classification of DNET.