苯丙酮尿症儿童的特殊饮食

Special Diet for Children with Phenylketonuria

苯丙酮尿症(Phenylketonuria,PKU)是一种遗传性疾病,人患病后身体代谢氨基酸苯丙氨酸的能力受到影响,导致苯丙氨酸在血液和大脑中积聚。PKU的主要治疗方法是低苯丙氨酸饮食,需要遵守某些饮食限制。为确保PKU儿童的健康成长,需对其实行严格的饮食管理。本文总结了PKU儿童的特殊饮食原则、方法以及需要注意的问题,以供参考。

Phenylketonuria(PKU)is a genetic disease that affects the body’s ability to metabolize the amino acid phenylalanine,leading to the accumulation of phenylalanine in the blood and brain.The main treatment method for PKU is a low phenylalanine diet,which requires adherence to certain dietary restrictions.To ensure the healthy growth of PKU children,strict dietary management is necessary.This article summarizes the special dietary principles,methods,and precautions for PKU children for reference.