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多学科团队协作诊治Cronkhite-Canada综合征一例

Diagnosis and therapy for a case of gastrointestinal hamartomatous polyp syndrome by the cooperation of multidisciplinary team
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摘要 本文报道1例罹患Cronkhite-Canada综合征(CCS)的22岁患者,接受足量糖皮质激素、硫唑嘌呤治疗后,患者的临床症状缓解,胃肠镜下息肉较治疗前明显好转。本文结合病例讨论CCS的发病机制、诊断、治疗及预后,以期为临床医师提供诊治经验。 A case of 22 year-old man with Cronkhite-Canada syndrome who responded to adequate glucocorticoids and azathioprine was reported.The pathogenesis,diagnosis,treatment and prognosis of Cronkhite-Canada syndrome were also discussed in details in order to provide clinical experience for clinicians.
作者 徐秋实 张润丰 金丽鑫 唐颢 徐天铭 周炜洵 王涛 李景南 李骥 Xu Qiushi;Zhang Runfeng;Jin Lixin;Tang Hao;Xu Tianming;Zhou Weixun;Wang Tao;Li Jingnan;Li Ji(Department of Gastroenterology,Peking Union Medical College Hospital,Peking Union Medical College,Chinese Academy of Medical Sciences,Beijing 100730,China;Department of Gastroenterology,People′s Hospital of Rizhao City,Rizhao 276800,China;Department of Pathology,Peking Union Medical College Hospital,Peking Union Medical College,Chinese Academy of Medical Sciences,Beijing 100730,China;Department of Dematology,Peking Union Medical College Hospital,Peking Union Medical College,Chinese Academy of Medical Sciences,Beijing 100730,China)
机构地区 中国医学科学院北京协和医学院北京协和医院消化内科 山东省日照市人民医院消化内科 中国医学科学院北京协和医学院北京协和医院病理科 中国医学科学院北京协和医学院北京协和医院皮肤科
出处 《中华炎性肠病杂志（中英文）》 2023年第4期375-378,共4页 Chinese Journal of Inflammatory Bowel Diseases
基金 北京协和医院中央高水平医院临床科研专项(2022-PUMCH-A-073) 中国医学科学院医学与健康科技创新工程项目(CIFMS#2021-I2M-1-003) 北京市大学生创新项目(202010023045)。
关键词 CRONKHITE-CANADA综合征 糖皮质激素 硫唑嘌呤 Cronkhite-Canada syndrome Glucocorticoid Azathioprine
分类号 R597 [医药卫生—内科学] R57 [医药卫生—消化系统]
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中华炎性肠病杂志（中英文）
2023年 第4期

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