原发性前列腺滑膜肉瘤1例报告

Primary renal synovial sarcoma:a case report

原发性前列腺滑膜肉瘤(PPSS)临床罕见。2021年5月宁波大学附属第一医院收治1例。患者31岁,因体检发现盆腔占位人院。术前盆腔增强MR、PET-CT和术前穿刺病理检查提示盆腔软组织肉瘤可能性大。行机器人辅助盆腔肿物根治性切除术。结合术后病理、免疫组化染色检查和基因检测确诊为单向型PPSS。术后1个月行异环磷酰胺+多柔比星辅助化疗,术后5个月行质子重离子辅助放疗。随访2年余,患者一般情况良好,影像学检查未见复发转移。

Primary prostate synovial sarcoma(PPSS)is rare in clinic.One patient was admitted to our hospital in May 2021.The patient was admitted to the hospital because of the physical examination.Preoperative pelvic enhanced MR,PETCT and preoperative puncture pathology suggested that pelvic soft tissue sarcoma was likely.Robot-assisted radical resection of pelvic tumor was performed,and the unilateral PPSS was diagnosed by postoperative pathology,immunohistochemistry and gene detection.Patients were treated with ifosfamide+adriamycin adjuvant chemotherapy one month after operation,and Proton therapy radiotherapy five months after operation.Follow-up for more than 2 years showed that the patients were generally in good condition,and no recurrence or metastasis was found in imaging.