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磁共振成像在亨廷顿病诊断中的应用价值 被引量:6

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摘要 亨廷顿病(Huntington disease,HD)的磁共振成像诊断国内尚未见报道,现对9例HD病人磁共振成像资料的对照研究报道如下。1 资料1.1 一般资料:研究组:1999年1月至2000年4月北京功能神经外科研究所收治的9例病人,年龄43—54岁,平均(47.3±11.1)岁,男性6例,女性3例,7例病人有明确的家族史。对照组:宣武医院健康体检的成年人8例,年龄40—62岁,平均(48.5±10.2)岁。男:女比例为1:1。1.2 诊断标准:①临床表现为后天出现、隐袭起病的、呈进行性加重的舞蹈样动作;②进行性智力减退,经简易智能量表(mini-mental state examination,MMSE)评分为22.6±1.6。
出处 《中国神经精神疾病杂志》 CAS CSCD 北大核心 2002年第6期430-430,435,共2页 Chinese Journal of Nervous and Mental Diseases
基金 本课题由国家科委资助(编号:96-610-05-17)
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参考文献2

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同被引文献57

  • 1左伋,夏蓓莉,陈秀珍,李采娟.中国人Huntington舞蹈病发病情况的初步研究[J].中国神经精神疾病杂志,1994,20(4):221-222. 被引量:5
  • 2张宝荣,殷鑫浈,夏昆,包颖颖,胡正茂,田均,刘志蓉,夏家辉.舞蹈病家系临床、影像学特征及基因突变分析[J].中华神经科杂志,2005,38(11):686-689. 被引量:7
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