获得性囊性肾病相关性肾细胞癌伴破裂出血及尿漏1例

One case of acquired cystic kidney disease-associated renal cell carcinoma with ruptured bleeding and urinary leakage

获得性囊性肾病相关性肾细胞癌(ACKD-RCC)是发生于获得性囊性肾病患者最常见的肾细胞癌类型。鉴于该肿瘤组织病理学独特,2016版世界卫生组织(WHO)肾脏肿瘤分类将其列为新增的肾细胞癌亚型之一。目前,关于该肿瘤的报道较少且多为个案报道,本文报道1例ACKD-RCC,通过查阅相关文献分析总结其临床病理学特征,旨在提高对该少见肾细胞癌亚型的认识。

Acquired cystic kidney disease-associated renal cell carcinoma(ACKD-RCC)is the most common type of renal cell carcinoma that occurs in patients with acquired cystic kidney disease.Due to the unique histopathology of this tumor,it is listed as one of the newly added renal cell carcinoma subtypes in the 2016 edition of the WHO Classification of Renal Tumors.At present,there are few reports on this tumor and most of them are case reports.This paper reports a case of ACKD-RCC,and summarizes its clinicopathological features by referring to relevant literatures,in order to improve the understanding on this rare subtype of renal cell carcinoma.