肺淋巴管平滑肌瘤病一例并文献复习

A case of pulmonary lymphangioleiomyomatosis and literature review

肺淋巴管平滑肌瘤病(PLAM)发病率低,在临床上属于少见病,因其起病隐匿,无典型症状,影像学表现易与肺气肿混淆,在临床上容易漏诊、误诊。本例患者因咳嗽进行体检时偶然发现胸腔积液及双肺多发囊腔影,经肺活检明确诊断该病。本文通过对该病例的病史、辅助检查、诊断过程进行分析及对相关文献资料复习,总结出PLAM一些临床特征及治疗经验,以期提高广大医务工作者对该类疾病的诊疗水平。

Pulmonary lymphangioleiomyomatosis(PLAM)has a low incidence and is a rare disease in clinical practice.Because of its insidious onset,no typical symptoms,imaging findings are easily confused with emphysema,it is easy to be missed and misdiagnosed in clinical practice.In this case,hydrothorax and multiple cystic shadows in both lungs were accidentally found during physical examination due to cough,and the disease was clearly diagnosed by lung biopsy.Through the analysis of the medical history,auxiliary examination,diagnosis process of the case and the review of relevant literature,this paper summarizes some clinical characteristics and treatment experience of PLAM,in order to improve the diagnosis and treatment level of the majority of medical workers.