Zinner综合征3例报告及文献复习

Zinner syndrome:a report of 3 cases and literatures review

目的 探讨Zinner综合征的临床特征、诊断、鉴别诊断及治疗方法。方法 回顾本院近年收治的3例Zinner综合征患者,根据该类患者的临床表现、诊治过程,结合文献对该病的临床特征和治疗后随访结果进行分析。结果 3例患者中2例为右侧病变,1例为左侧病变;3例均无射精障碍,2例为成年患者,已育。临床确诊后,1例排尿困难者行经腹腔镜下精囊囊肿去顶及输尿管残端切除术,1例合并精囊结石的无症状患者行精囊镜取石术,1例无症状患者仅采取随访观察。2例手术均顺利完成,无并发症。术后复查,影像学较术前改善,排尿困难的患者症状消失。结论 一侧肾缺如合并同侧盆腔囊性占位,需要考虑Zinner综合征的可能。应根据患者具体表现选择个体化治疗方法,对符合手术适应证的患者可采用腹腔镜手术或经尿道手术。

Objective To investigate the clinical features,diagnosis,differential diagnosis and treatment of Zinner syndrome.Methods Three patients with Zinner’s syndrome admitted in our hospital in recent years were reviewed.According to the clinical manifestations,diagnosis and treatment process of these patients,combined with the relevant literatures,the clinical characteristics and follow⁃up results after treatment of this disease were summarized and analyzed.Results Among the 3 patients,2 patients had right side lesions and 1 patient had left side lesions.All the patients had no ejaculatory disorder.Two adult patients had given birth.After clinical diagnosis,one patient with dysuria underwent laparoscopic seminal vesicle cyst decapitation and ureterectomy,and one asymptomatic patient combined with seminal vesicle stones received seminal vesicle lithotomy,and the other asymptomatic patient was only followed up.The operations were all successfully completed and no complications occurred.The postoperative reexamination showed that their imaging results were all improved,and the symptoms of the patient with dysuria disappeared.Conclusion The possibility of Zinner syndrome should be considered in the patients with one kidney absence and ipsilateral pelvic cystic lesion.Individualized treatment should be selected according to the specific performance of patients.Laparoscopic surgery or transurethral surgery could be used for patients who have the surgical indications.