幼儿鼻内型鼻神经胶质异位1例报告

The intranasal type of nasal glial heterotopia in infant:one case report

鼻神经胶质异位(nasal glial heterotopia,NGH)又称鼻神经胶质瘤,是一种罕见的先天性发育异常。扬州大学附属医院在2023年收治1名2岁鼻内型鼻神经胶质异位女性患儿,因双侧间断流涕就诊于我院耳鼻咽喉头颈外科门诊,检查见左侧鼻腔占位,拟诊“鼻腔占位(左)”收治入院,完善相关检查后行手术治疗,术后病理检查结果示胶质瘤,最终诊断为鼻神经胶质异位鼻内型,术后随访半年,未见复发,无脑膜炎及脑脊液鼻漏等并发症。NGH发病率极低,容易漏诊,对于儿童先天性鼻中线部位肿物,CT结果提示肿物与颅内不相通时应考虑本病可能,及时手术治疗预后良好。

Nasal glial heterotopia(NGH),formerly known as nasal glioma,is a rare congenital developmental abnormality.A two-year-old female infant with intranasal NGH was admitted to Affiliated Hospital of Yangzhou University in 2023.The patient treated in the Department of Otorhinolaryngology Head and Neck Surgery in our hospital due to bilateral runny nose.Finding a nasal space occupying lesion in the left nasal cavity,she was hospitalized as“nasal space occupying lesion(left)”.Consequently,she underwent surgical treatment after completing the relevant examinations.The postoperative pathological examination results showed it was glioma,and then she was diagnosed with intranasal type of nasal glial heterotopia finally.After half a year of postoperative follow-up,there was no recurrence and complications such as meningitis and cerebrospinal fluid rhinorrhea.The incidence of NGH is very low,and it is easy to miss diagnosis.For congenital nasal midline tumors in children,NGH should be considered when CT results suggest the tumor is not communicated with the skull,which has a good prognosis after surgical treatment.