POMES综合征误诊为肝硬化1例

Misdiagnosis of POEMS syndrome as liver cirrhosis:a case report

POMES综合征是一种罕见的累及神经、血液、内分泌、皮肤、浆膜腔等多系统损害的综合征,临床表现多样,存在一定的临床异质性,加之临床医生对本病缺乏必要的认识,易被误诊、漏诊。本文报道1例因脾大、腹水、食管胃底静脉曲张误诊为肝硬化的POMES综合征,随访资料完整,通过对该病例诊治过程的分析,以期提高临床医师对该病的认识,避免误诊、漏诊,做到早诊断、早治疗。

POMES syndrome is a rare syndrome involving nerve,blood,endocrine,skin,serous cavity and other multi-system damage.On account of the various clinical manifestations and heterogeneity,coupled with the lack of necessary understanding of the disease by clinicians,it is easy to be misdiagnosed and missed diagnosis.This paper reported a case of POMES syndrome misdiagnosed as liver cirrhosis due to spleen enlargement,ascites,esophageal and gastric varices.The follow-up data was complete.It is hoped to improve clinicians’understanding of POMES syndrome through the analysis of the diagnosis of this case,so as to avoid misdiagnosis and missed diagnosis,and achieve early diagnosis and treatment.