致心律失常心肌病影像学研究进展

Progress in imaging research on arrhythmogenic cardiomyopathy

致心律失常心肌病是一种以纤维脂肪性心肌替代为病理特征的疾病,其可累及右心室、左心室及双心室。该疾病目前尚无诊断金标准,主要根据心脏的结构、组织学、心电图、心律失常和家族特征等多模态的方案进行诊断。目前也无特定的治疗,临床上主要专注于心律失常风险分层并对其进行相应的临床管理,影像学技术在致心律失常心肌病的诊断和管理中起着关键作用。本文将对致心律失常心肌病影像学研究进展进行综述,以期为临床医生的诊疗工作提供参考。

Arrhythmogenic cardiomyopathy is a disease characterized by fibrous and fatty myocardial replacement,which can affect the right ventricle,left ventricle,and both ventricles.There is currently no gold standard for diagnosis of this disease,and the diagnosis is performed mainly based on multimodal protocols such as heart structure,histology,electrocardiogram,arrhythmia,and family characteristics.At present,there is no specific treatment for the disease,and in clinical practice,the main focus is on stratification of arrhythmia risk and corresponding clinical management.Imaging technology plays a key role in the diagnosis and management of arrhythmogenic cardiomyopathy.This article will review the progress of imaging research on arrhythmogenic cardiomyopathy,in order to provide reference for the diagnosis and treatment of clinical doctors.