肝脏原发性腺样囊性癌一例并文献复习

Primary Adenoid Cystic Carcinoma of the Liver:A Case Report and Literature Review

目的通过报告肝脏原发性腺样囊性癌的病例,增进医学界对这种疾病的认识。方法针对我院1例肝脏原发性腺样囊性癌患者进行鉴别分析,描述其组织病理学特征和免疫组化概况及整个诊疗过程,并回顾了相关文献。结果判定本例患者确定是肝脏原发腺样囊性癌,国内外仅有2例类似病例。结论肝脏原发性腺样囊性癌早期临床表现无特异性,易延误诊治,远处转移对患者生存影响较大,早期明确诊断后应及时行手术治疗。

Objective To report the case of primary adenoid cystic carcinoma of the liver and enhance the medical community's understanding of this disease.Methods A case of primary adenoid cystic carcinoma of the liver in our hospital was analyzed and histopathological characteristics and immunohistochemical profile as well as the entire diagnosis and treatment process were described,and relevant literature was reviewed.Results This patient was determined to have primary adenoid cystic carcinoma of the liver,and there were only two similar cases in China and abroad.Conclusion The early clinical manifestations of primary adenoid cystic carcinoma of the liver are non-specific,which can easily delay diagnosis and treatment.Distant metastasis has a greater impact on the survival of patients.Surgical treatment should be performed in a timely manner after early diagnosis.