内听道狭窄伴脑白质异常患儿人工耳蜗植入术后康复效果

The Effect of Cochlear Implantation in Children With Internal Auditory Canal Stenosis and White Matter Abnormalities

目的探讨人工耳蜗植入术对内听道狭窄伴脑白质异常患儿的听觉言语康复效果。方法通过对1例内听道狭窄伴脑白质异常患儿2年康复期内的声场下助听听阈、林氏六音测试、听觉语言能力、听觉行为分级(CAP)和言语可懂度分级(SIR)的阶段性评估结果进行追踪,分析其听觉言语能力。结果患儿人工耳蜗术后左右耳助听听阈稳定期存在差异,右耳不能辨识林氏六音及言语,康复2年后其听觉能力及语言能力均达到二级,听觉行为达5级,言语可懂度达3级。结论人工耳蜗植入术可提高内听道狭窄伴脑白质异常患儿的听觉言语能力,针对患儿的特殊性,需灵活运用康复教学方法,从而提高康复质量。

Objective To explore the effect of cochlear implantation on the rehabilitation of hearing and speech in children with internal auditory canal stenosis and white matter abnormalities.Methods The hearing and speech ability of a child with internal auditory canal stenosis and cerebral white matter abnormality in the rehabilitation period of 2 years were analyzed by tracing the results of sound field hearing threshold,Ling's six sounds test,auditory language ability,categories of auditory performance(CAP)and speech intelligibility rating(SIR),and the staged evaluation of her learning ability.Results There is a difference in the stuble hearing threshold between the left and right ears of the child after CI,and the right ear cannot recognize the Ling's six sounds and speech after 2 years,the hearing and language abilities of the child reached Grade 2,the auditory behavior reached Grade 5,and the speech intelligibility reached Grade 3.Conclusion Cochlear implantation can improve the hearing and speech ability of children with internal auditory canal stenosis and white matter abnormalities.According to the particularity of children,it is necessary to flexibly use rehabilitation teaching methods to improve the quality of rehabilitation.