血友病患者出血急诊管理中国指南(2024年版)

Chinese guidelines for emergeney management of bleeding in hemophilia patients(2024)

血友病是一种X染色体连锁的隐性遗传性出血性疾病。出血是血友病患者最常见的急症,也是血友病患者致死、致残、影响生活质量的主要因素。快速识别和规范处置对于改善患者预后具有重要意义。急诊科是血友病患者出血的主要首诊科室,血友病出血急诊处置流程复杂,常常需要多学科联合诊疗和综合管理。为了规范国内从事血友病诊疗的各相关科室的诊疗行为,中华医学会血液学分会血栓与止血学组和中国血友病协作组共同制定了本指南。

Hemophilia is a X-linked recessive hemorrhagic disease.Bleeding is the most common complication of hemophilia,and it is also the main cause leading to death and disability or reducing the quality of life of hemophilia patients.Rapid identification and standardized management of the bleeding events is of great significance to improve the prognosis of hemophilia patients.Emergency department is the frontline department for hemophilia patients with bleeding.The emergent management process of hemophilia hemorrhage is complex and often needs multidisciplinary team cooperation.To increase the awareness of the related professionals who may involve in the management of bleeding events of hemophilia patients,in collaboration with the Thrombosis and Hemostasis Group,Chinese Society of Hematology,Chinese Medical Association,Hemophilia Treatment Center Collaborative Network of China issued the Chinese guidelines for emergency management of bleeding in hemophilia patients.