中枢神经系统血管母细胞瘤的诊治进展

Progress in diagnosis and treatment of hemangioblastoma of the central nervous system

血管母细胞瘤是一种较为罕见的中枢神经系统良性肿瘤。它既可散发,亦可作为von Hippel-Lindau(VHL)病的一部分出现,约占颅内肿瘤的2%,占原发性脊髓肿瘤的2%~10%。影像学检查是术前诊断血管母细胞瘤的重要手段,而最终确诊需要依赖于病理诊断。目前,血管母细胞瘤的主要治疗方法为显微手术,病死率较低,远期手术效果良好。近年来,随着研究的深入,临床对于血管母细胞瘤有了新的认识。本文就中枢神经系统血管母细胞瘤的诊治进展作一综述,为临床诊治血管母细胞瘤提供参考。

Hemangioblastoma is a relatively rare benign tumor of the central nervous system.It can occuRsporadically or as part of von Hippel-Lindau(VHL)disease,accounting for approximately 2%of intracranial tumors and 2%~10%of primary spinal cord tumors.Imaging examinations are important means for preoperative diagnosis of hemangioblastoma,while the final diagnosis relies on pathological diagnosis.Currently,the main treatment for hemangioblastoma is microsurgery,which has a low mortality rate and favorable long-term surgical outcomes.In recent years,with in-depth research,there have been new insights into hemangioblastoma in clinical practice.This article presents a review of the progress in the diagnosis and treatment of hemangioblastoma of the central nervous system,providing a reference for the clinical diagnosis and treatment of hemangioblastoma.