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遗传性球形红细胞增多症与带3蛋白的相关性研究进展 被引量：6

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摘要 遗传性球形红细胞增多症（hereditary spherocytosis,HS）是一种由红细胞膜缺陷所致的溶血性疾病。外周血涂片见小球形红细胞显著增多,中央淡染区消失。典型临床表现为不同程度的黄疸、脾大、红细胞脆性增加及贫血。其为遗传性溶血性贫血中发病率最高的疾病,在北欧和北美地区,HS发病率高达1/2 000,也是日本常见的先天性溶血性贫血[1]。有欧洲学者对300例HS患者进行红细胞膜蛋白测定,
作者 马诗玥 韦红英 林发全
机构地区 广西医科大学第一附属医院检验科
出处 《广东医学》 CAS 北大核心 2016年第18期2843-2845,共3页 Guangdong Medical Journal
基金 国家自然科学基金资助项目(编号:81360263)
关键词 红细胞膜蛋白 小球形红细胞 红细胞脆性 溶血性疾病 欧洲学者 外周血涂片 细胞结构 脾大 地中海贫血筛查 脾切除手术
分类号 R5 [医药卫生—内科学]
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参考文献15

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同被引文献29

引证文献6

二级引证文献21

广东医学
2016年 第18期

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