原发性肾脏肉瘤的诊治探讨

Diagnosis and treatment of primary renal sarcoma

目的 探讨进一步提高原发性肾脏肉瘤的诊断、治疗水平及改善硕后。方法 对1992/2001收治的6例3种肾脏原发肉瘤采用回顾性分析研究,结合国内外文献报道的诊治进展进行深入讨论和分析。结果 6例均行根治性肾切除术,术后病理证实平滑肌肉瘤3例,横纹肌肉瘤1例,恶性横纹肌样瘤2例。生存期3～27(平均15.8)月。结论 原发性肾脏肉瘤的恶性度高,较易发生转移,预后差。早期诊断,综合治疗能够显著改善预后,延长生存期。

AIM To improve early diagnosis, treatment and prognosis of primary renal sarcoma. METHOD Combining modern progress on diagnosis and treatment of primary renal sarcoma, we retrospectively analyzed and discussed the data of 6 patients with primary renal sarcoma (3 types), who were admitted in our hospital from 1992 to 2001. RESULTS Radical nephrectomy was performed in all 6 patients and leiomyosarcoma in 3 patients ,malignant rhabdomyoid tumor in 2,and rhabdomyosarcoma in 1 were demonstrated by pathologic examination. The survival time was 3 - 27(mean 15.8) months.CONCLUSION Primary renal sarcoma is characterized by high malignancy,early metastasis , and poor prognosis. Early diagnosis and appropriate combining tlierapy may improve the prognosis and survival of patients with primary renal sarcoma.