附睾乳头状囊腺瘤伴睾丸萎缩1例报告

Papillary Cystadenoma of the Epididymis Accompanied by Testicular Atrophy: One Case Report

附睾乳头状囊腺瘤是一种少见的良性肿瘤 ,可能与vonHippel Lindau综合征并存。本文报告 1例附睾乳头状囊腺瘤病例 ,男性 ,38岁 ,瘤体位于右侧附睾全段 ,呈球形包块状 ,大小约 5 .0cm× 4 .0cm× 4 .0cm ,包膜完整 ,病理检查可见典型乳头样增生的腺样结构及高柱状透亮粘液腺细胞 ,部分腺腔见胶质样嗜酸性物质。

Papillary cystadenoma of the epididymis is a rare benign tumor, accounting for only 4 per cent of all epididymal tumors. Histologically, it can be confused with metastatic renal cell carcinoma.This extremely rare lesion may occur sporadically or as a manifestation of von Hippel Lindau(VHL) disease. The present paper reported a case of papillary cystadenoma accompanied by testicular atrophy with no signs of VHL syndrome or infertility. To date, no similar case was reported in the literature.The tumor measured 5.0 cm× 4.0 cm × 4.0 cm and was located in the right epididymis. Histopathologic examination of a surgically removed specimen indicated a primary papillary cystadenoma.Histomorphologically, these tumors are characterized by cysts with colloid like contents and papillary formations of light epithelium. Since metastatic renal cell carcinoma may be histologically similar to papillary cystadenoma, the importance of long term urologic follow up for possible presentation of renal cell carcinoma is discussed.