摘要
Background: Degos disease is a rare systemic disorder with involvement of the skin and visceral organs, leading to death in about 50%of cases within 1 or 2 years. In recent years, several cases with cutaneous lesions only have been recog nized. Methods: We report on a young male patient presenting with single inconsp icuous papules with bluish/black centres on the trunk and the upper limbs that, upon healing turnwhite. These lesions recurred on different locations over the p ast 6 years, and were never more than two to three at one time. Results: Histopa thological examinations revealed archetypal features for Degos disease. The pati ent had no other complaints, neither visceral organs nor the central nerve syste m were involved. Laboratory examinations were within normal range. Conclusions: This case increases the number of reports on a benign course of Degos disease. It raises the question if the “malignant”and the “benign”course of the disease represent two distinct diseases or variants of a systemic vasculitis with unkn own cause.
Background: Degos disease is a rare systemic disorder with involvement of the skin and visceral organs, leading to death in about 50%of cases within 1 or 2 years. In recent years, several cases with cutaneous lesions only have been recog nized. Methods: We report on a young male patient presenting with single inconsp icuous papules with bluish/black centres on the trunk and the upper limbs that, upon healing turnwhite. These lesions recurred on different locations over the p ast 6 years, and were never more than two to three at one time. Results: Histopa thological examinations revealed archetypal features for Degos disease. The pati ent had no other complaints, neither visceral organs nor the central nerve syste m were involved. Laboratory examinations were within normal range. Conclusions: This case increases the number of reports on a benign course of Degos disease. It raises the question if the “malignant”and the “benign”course of the disease represent two distinct diseases or variants of a systemic vasculitis with unkn own cause.
