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Anderson Fabry病的心脏损害及治疗 被引量:1

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摘要 Anderson Fabry病(AFD)是X性染色体显性遗传疾病,国内未见报道.患者通常有多器官损害,心脏损害尤其常见,可发生进展性肥厚型心肌病、瓣膜病、心律失常,亦可导致冠心病.目前在各种原因所致的肥厚型心肌病中,只有AFD导致的肥厚型心肌病可进行病因治疗.现就AFD患者的心脏病变以及α-galA酶替代疗法作一概述.
作者 安丰双 张运
出处 《山东医药》 CAS 北大核心 2003年第31期65-66,共2页 Shandong Medical Journal
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