致心律失常性右室心肌病的临床特征及预后因素

Clinical Features and Prognostic Factors of Arrhythmogenic Right Ventricular Cardiomyopathy

致心律失常性右室心肌病又称致心律失常性右室发育不良,是一种右室心肌细胞被纤维/脂肪细胞取代,进而导致室性心律失常的遗传性心肌病。致心律失常性右室心肌病主要的发病人群以青少年为主,以年轻运动员最为多见。近些年随着医学水平的进步,对致心律失常性右室心肌病的临床特征和预后因素等方面的认识越来越深入。现就致心律失常性右室心肌病的临床特征及其预后因素进行综述,为致心律失常性右室心肌病的临床治疗提供帮助。

Arrhythmogenic right ventricular cardiomyopathy(ARVC),also known as arrhythmogenic right ventricular dysplasia,is a genetic cardiomyopathy of ventricular arrhythmia caused by the replacement of right ventricular myocytes by fibro/fatty cell. The main morbidity groups are adolescents,and the young athletes are the most common. In recent years,with the advancement of medical level,the clinical characteristics and prognostic factors of ARVC have become more and more in-depth. This article reviews the clinical features of ARVC and its prognostic factors,and provides assistance for the clinical treatment of ARVC.