摘要
多灶性运动神经病 (multifocal motorneuropathy,MMN)是近年来新被认识的一种神经疾病。表现为进行性、非对称性肢体运动无力 ,以远端为重。免疫学检查部分患者抗 -神经节苷脂 (GM1 )抗体滴度升高。电生理检查以持续性、节段性运动神经传导阻滞 (PMCBs)为特征。病理学检查发现传导阻滞部位有慢性脱髓鞘改变。激素治疗无效 ,环磷酰胺及大剂量免疫球蛋白等治疗有效。
出处
《中国神经免疫学和神经病学杂志》
CAS
2003年第2期133-136,共4页
Chinese Journal of Neuroimmunology and Neurology
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