软骨粘液样纤维瘤12例临床分析

Clinical Analysis of Chrondromyxoid Fibroma (in 12 cases)

目的 :为提高对这种少见良性骨肿瘤的认识和诊断水平。方法 :收集经病理证实的软骨粘液样纤维瘤 12例 ,分析了该肿瘤的临床表现和各种不同部位的X线表现。结果 :①临床表现 :以局部疼痛为主 ,可有肿胀感 ,发热感。②X线表现 :多发生于下肢长管状骨 ,好发于干骺端 ,呈偏心性膨胀性生长 ,圆或椭圆形 ,可分叶 ,出现骨嵴和钙化 ,边缘硬化 ;发生于短管状骨者 ,为中心性膨胀性生长 ,骨皮质变薄 ;发生于肩胛骨者 ,呈圆形骨破坏区 ,边缘清晰 ,有轻度硬化和膨胀 ;发生于肋骨者 ,沿肋骨长轴生长 ,呈蜂窝状膨胀性生长 ,可出现钙化。结论 :软骨粘液样纤维瘤具有一定特点 ,掌握这些特点 ,可以提高对这种少见骨肿瘤的认识和诊断水平。

Objective: To deepen our understanding about the chrondromyxoid tibroma and raise our diagnostic level about this lesion. Method: 12cases verified by pathology were evaluated,their clinical characterstics and the different radiographic manifestation locatedthe different bone. Result: ①Clinical characteristics: Local pain was main clinical manifestation , local sweiling and slight fever could be showalso. ②Radiographic manifestation: In long tubular bone chrondromyxoid tibroma of frequent occurrence than others, the lesion often located at the metaphsis ,and was a round or oval eccentric expansive destruction of bone, lobulated msrgins, septalion and sclerotic rim, calcium was seen in involved area; in short tubular bone, the lesion was centric bulk, and the cortex of involved bone was thining; in scapula, the lesion was rond bone destruction, distinct margins, expansive and slight sclerotic rim; in rib , the lesion was malticystic and bulk, and was growing along the rib axis, caleium could be showed in involved area. Conclusion: the chrondromyxoid fibroma has a feature on X-film, it is belpful to deepen our understanding and raise our diagnostic level to this rare bone tumor.