Sturge-Weber综合征CT诊断(附12例分析)

Diagnosis of Sturge-Weber syndrome on CT:analysis of 12 cases

目的:探讨Sturge-Weber综合征的CT表现和诊断价值。方法:回顾性分析12例Sturge-Weber综合征的CT表现。结果:12例均有脑皮层小片状到“脑回状”钙化。其中右侧6例,左侧5例,1例为两侧额、顶、颞、枕叶广泛钙化;脑萎缩10例;颅骨增厚4例;1例增强扫描示钙化灶周围皮层表面“脑回状”强化。结论:Sturge-Weber综合征颅内皮层钙化具有一定CT特征;典型的临床及CT表现可以确诊本病;有颅面部血管瘤而CT平扫阴性时应复查。

Objective:To investigate CT manifestations of Sturge-Weber syndrome and its diagnostic value.Materials and Methods:12cases of Sturge-Weber syndrome examined with CT were retrospectively analyzed.Results:Patchy shape and*/or gyriform cortical calcifications were seen in all12cases.The foci of cortical calcification(n=12)which located in right hemisphere in6cases,left in5cases and located in frontal,parietal,temporal,occipital lobe of both hemisphere in one case.Cerebral atrphy(n=10);Thickening of the cranium(n=4);'gyriform'enhancement in the surface parenchyma adjacent to cortical calcification occurred in one case on enhanced CT.Conclusion:The cortical calcification of Sturge-Weber syndrome has some characteristics;CT combined with clinical data can correctly make the diagnosis of Sturge-Weber syndrome .If the CT findings of cerebral parenchyma is negative but the patient has facial angioma involving the area of trigeminal nerve distribu-tion,then CT reexamination is required.