婴幼儿心内膜弹力纤维增生症的诊断(附43例报告)

The Diagnosis of Endocardial Fibroelastosis in Children

目的 :进一步认识心内膜弹力纤维增生症诊治的意义。方法 :对本院儿科收治的心内膜弹力纤维增生症 4 3例 ,于住院后作心电图、X线心脏摄片及二维和 /或多普勒心脏超声检查。结果 :本组 4 3例均有心脏形态学改变 ,表现心脏增大以左心室增大为主 ;超声心动图尚显示心内膜呈弥漫或不规则增厚达 3～ 6 mm。结论 :1岁以内患儿突发心力衰竭者 ,超声心动图检查必不可少 ,对临床诊断有肯定价值。

Objective:To explore the diagnosis of endocardial ribroelastosis(EFE) in children.Methods:Forty-three cases of EFE were diagnosised in The First Hospital of Huangshi City.Teh clinical data included electrocardiogram,X-ray sternum and echocardiography.Results:All of 43 cases had cordis micphological changes, dominating changes were augmetation of left ventricle.Echocardiography found the diffused or anomalistic incrassation of endocardium (3～6 mm).Conclusion:In infant with saddened heart failure,echocardiography is important and significant in the diagnosis of EFE.