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以急性溶血性贫血为首发表现的Wilson病1例 被引量:1

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摘要 目的:认识Wilson病(WD)临床表现的多样性. 方法:报告1例以急性溶血性贫血(溶贫)为首发表现的WD,并行文献复习. 结果和结论:以急性溶血为首发症状是WD一种少见的起病形式,常伴肝衰竭,预后不佳;WD误诊率较高主要与临床表现复杂多样有关,对于年轻的不明病因的溶贫患者应注意排除WD的可能;血清碱性磷酸酶活性下降对诊断有一定帮助.
出处 《世界华人消化杂志》 CAS 2004年第5期1257-1258,共2页 World Chinese Journal of Digestology
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