小肠肠系膜韧带样纤维瘤病1例

Mesenteric Desmoid-Type Fibromatosis of the Small Intestine

目的:小肠肠系膜韧带样纤维瘤病是一种罕见病,临床术前诊断通常容易误诊。本研究通过病理报道分析该疾病临床症状、影像特点及病理特征,回顾性分析并进行总结,旨在增加对该病的影像和临床认识,促进疾病的治疗及改善预后。方法:报道1例发生在腹腔内的小肠肠系膜处的韧带样纤维瘤病。结果:根据临床表现、CT检查及病理结果,诊断为小肠肠系膜韧带样纤维瘤病。结论:韧带样纤维瘤病发生率低,腹腔内发病者罕见,起病隐匿,肿瘤生长缓慢但腹腔内型一般体积较大,术前诊断通常容易误诊。

Objective: Ligamentoid fibromatosis of small intestine mesentery is a rare disease, which is usually misdiagnosed before clinical operation. This study analyzed the clinical symptoms, imaging features, and pathological features of the disease through pathological reports, and made a retrospective analysis and summary, aiming to increase the imaging and clinical understanding of the disease, promote the treatment of the disease and improve the prognosis. Methods: A case of desmoid fi-bromatosis of small intestine mesentery in the abdominal cavity was reported. Results: According to the clinical manifestation, CT examination, and pathological results, it was diagnosed as small in-testinal mesenteric ligament-like fibromatosis. Conclusion: The incidence of desmoid fibromatosis is low, the incidence in the abdominal cavity is rare, the onset is hidden, and the tumor grows slowly, but the intraperitoneal type is generally large, and the preoperative diagnosis is usually easy to be misdiagnosed.