摘要
Cutis laxa is a rare disease, related to loss of skin elasticity, which can be hereditary or acquired, with or without associated visceral damage. It is marked by great psychological and social repercussions. The purpose of this paper is to highlight a particular cause of neonatal occlusion: cutis laxa. We report a new observation about a case of cutis laxa hospitalized in the pediatric department at Mohammed V hospital in Tangier, admitted right after birth for the management of macrosomia with wrinkled and inelastic skin, suggesting the diagnosis of cutis laxa. The evolution that followed was marked by the occurrence of several occlusive episodes of a functional nature. Conclusion: visceral involvement in the cutis laxa is reported in several reviews. In our patient the neonatal occlusion was most likely related to her disease. The management of the case must be multidisciplinary.
Cutis laxa is a rare disease, related to loss of skin elasticity, which can be hereditary or acquired, with or without associated visceral damage. It is marked by great psychological and social repercussions. The purpose of this paper is to highlight a particular cause of neonatal occlusion: cutis laxa. We report a new observation about a case of cutis laxa hospitalized in the pediatric department at Mohammed V hospital in Tangier, admitted right after birth for the management of macrosomia with wrinkled and inelastic skin, suggesting the diagnosis of cutis laxa. The evolution that followed was marked by the occurrence of several occlusive episodes of a functional nature. Conclusion: visceral involvement in the cutis laxa is reported in several reviews. In our patient the neonatal occlusion was most likely related to her disease. The management of the case must be multidisciplinary.
