脾切除治疗小儿遗传性球形细胞增多症(附35例临床分析)

The Experiences of Splenectomy in 35 Cases of Hereditary Spherocytosis in Children

作者就35例脾切除治疗小儿遗传性球形细胞增多症的经验,分析和讨论了有关脾切除的年龄,手术注意事项以及合并胆结石的处理问题.

35 cases of hereditary spherocytosis (HS) were treated by splenectomy in the author's hospital from July 1974 to December 1985. 18 males and 17 females. The age sranged from 18 months to 14 years. Sixteen of them were between 4～6 years. All of them had jaundice, anemia and splenomegaly of various degree. Splenectomy was performed on all of the 35 cases. Accessory spleens were found in ten (32%) of the patients and all were removed. Gallstone was found in a girl and was removed. Postoperative courses were uneventfull in all. Twenty-eight cases were followed-up for 76.3 months ( mean of 13-142 months ) . All of them were symptom free，The age of splenectomy, cautions during operation, and the treatment of gallstone were discussed.