Binary Cu-based chalcogenide thermoelectric materials have attracted a great deal of attention due to their outstanding physical properties and fascinating phase sequence.However,the relatively low figure of merit z T...Binary Cu-based chalcogenide thermoelectric materials have attracted a great deal of attention due to their outstanding physical properties and fascinating phase sequence.However,the relatively low figure of merit z T restricts their practical applications in power generation.A general approach to enhancing z T value is to produce nanostructured grains,while one disadvantage of such a method is the expansion of grain size in heating-up process.Here,we report a prominent improvement of z T in Cu2Te(0.2)Se(0.8),which is several times larger than that of the matrix.This significant enhancement in thermoelectric performance is attributed to the formation of abundant porosity via cold press.These pores with nano-to micrometer size can manipulate phonon transport simultaneously,resulting in an apparent suppression of thermal conductivity.Moreover,the Se substitution triggers a rapid promotion of power factor,which compensates for the reduction of electrical properties due to carriers scattering by pores.Our strategy of porosity engineering by phonon scattering can also be highly applicable in enhancing the performances of other thermoelectric systems.展开更多
神经纤维瘤病Ⅱ型(neurofibromatosis type 2,NF2)是一种比较罕见的常染色体显性遗传疾病,其特征性表现为双侧前庭神经鞘瘤,另外还常常伴有皮下神经纤维瘤、晶状体后囊浑浊、脑膜瘤、室管膜瘤、胶质瘤、脊髓肿瘤等[1]。NF2致病基因位于...神经纤维瘤病Ⅱ型(neurofibromatosis type 2,NF2)是一种比较罕见的常染色体显性遗传疾病,其特征性表现为双侧前庭神经鞘瘤,另外还常常伴有皮下神经纤维瘤、晶状体后囊浑浊、脑膜瘤、室管膜瘤、胶质瘤、脊髓肿瘤等[1]。NF2致病基因位于染色体22q12.2,NF2基因突变导致其编码的merlin蛋白功能异常或缺乏从而引起肿瘤生长[2]。笔者现报道NF2一家系患者的临床特征、实验室检查、影像学特征、治疗及预后、基因突变特点等资料,以提高临床工作者对该病的认识。展开更多
基金Project supported by the National Natural Science Foundation of China(Grant Nos.51771126 and 11774247)the Youth Foundation of Science and Technology Department of Sichuan Province,China(Grant No.2016JQ0051)+2 种基金Sichuan University Outstanding Young Scholars Research Funding(Grant No.2015SCU04A20)the World First-Class University Construction Fundingthe Fundamental and Frontier Research Project in Chongqing(Grant No.CSTC2015JCYJBX0026)
文摘Binary Cu-based chalcogenide thermoelectric materials have attracted a great deal of attention due to their outstanding physical properties and fascinating phase sequence.However,the relatively low figure of merit z T restricts their practical applications in power generation.A general approach to enhancing z T value is to produce nanostructured grains,while one disadvantage of such a method is the expansion of grain size in heating-up process.Here,we report a prominent improvement of z T in Cu2Te(0.2)Se(0.8),which is several times larger than that of the matrix.This significant enhancement in thermoelectric performance is attributed to the formation of abundant porosity via cold press.These pores with nano-to micrometer size can manipulate phonon transport simultaneously,resulting in an apparent suppression of thermal conductivity.Moreover,the Se substitution triggers a rapid promotion of power factor,which compensates for the reduction of electrical properties due to carriers scattering by pores.Our strategy of porosity engineering by phonon scattering can also be highly applicable in enhancing the performances of other thermoelectric systems.
文摘神经纤维瘤病Ⅱ型(neurofibromatosis type 2,NF2)是一种比较罕见的常染色体显性遗传疾病,其特征性表现为双侧前庭神经鞘瘤,另外还常常伴有皮下神经纤维瘤、晶状体后囊浑浊、脑膜瘤、室管膜瘤、胶质瘤、脊髓肿瘤等[1]。NF2致病基因位于染色体22q12.2,NF2基因突变导致其编码的merlin蛋白功能异常或缺乏从而引起肿瘤生长[2]。笔者现报道NF2一家系患者的临床特征、实验室检查、影像学特征、治疗及预后、基因突变特点等资料,以提高临床工作者对该病的认识。