Oeis Syndrome (Cloacal Exstrophy): About Two Cases Treated at the Mother and Child Teaching Hospital in Cotonou (Benin)

Introduction: OEIS syndrome, the most severe form of exstrophy-epispadias complex, is characterized by the existence of an omphalocele, a bladder exstrophy, an anal imperforation and a spina bifida. Case Presentation: Two clinical cases admitted at the first day of life in neonatology department are reported;one was born by caesarean section, weighing 2500 g and the other one vaginally with a weight at 1890 g. The first child’s mother was a primigravid, primiparous and the second mother was multiparous. Prenatal ultrasound was performed in one case. The clinical examination found two exstrophied hemi-bladders with two productive ureteral meatus, separated by a double intestinal orifice, a manifestation of anal imperforation, omphalocele, spina bifida and lumbar vertebral malformations;which corresponds to a typical form of OEIS syndrome. One of the babies had an associated clubfoot. The karyotype could not be performed. Both were dead;the first in the early postoperative period, the second one at 16 days of life without surgery. Conclusion: OEIS syndrome is a rare condition and represents a therapeutic challenge in developing countries. Promoting prenatal diagnosis is essential.

Are multidisciplinary consultation meetings for prenatal diagnosis achievable in a low-income country? A descriptive cross-sectional survey in Benin

Objective The multidisciplinary antenatal diagnosis staff bring together practitioners who are involved in the management of the antenatal period at birth.This project was designed following the French experience to institute multidisciplinary consultation meetings for prenatal diagnosis(MCMPD)in Benin.Methods This is a descriptive cross-sectional study examining the knowledge,attitudes,and practices of Beninese practitioners in the field of MCMPD to develop the pilot phase of the project.Results We collected 108 participants from different specialties.Pediatricians and pediatric surgeons were in the majority at 23.9% and 16.5%,respectively.Sixty-seven percent of participants were from the public sector(n=75).One practitioner felt that it was not a good idea to implement these meetings.Almost all staff(96.2%)agreed that this meeting would have a positive impact on reducing neonatal mortality.Omphalocele(58.5%),spina bifida aperta(43.6%),and gastroschisis(34%)were the most commonly diagnosed antenatal conditions in Benin.No neonatal pathology required medical termination of the pregnancy according to 35.6% of the participants.Conclusions The objective of reducing infant mortality due to medical and surgical pathologies is a noble one and deserves to be supported.This innovative project,developed through this study,the first of its kind in the subregion,will contribute inexorably to the achievement of the third Goal Sustainable Development.