先天性食管闭锁成形术后22年发生的食管腺癌

Esophageal cancer development after previous atresia repair is extremely rare in young patients. We present the clinical course of a patient who developed an adenocarcinoma of the esophagus at the age of 22 years, after repair of a tracheoesophageal fistula with esophageal atresia in the neonatal period. She developed a stricture of the esophageal anastomosis requiring frequent dilatations. Six years after an antireflux procedure because of a difficult treatable severe gastroesophageal reflux, an advanced adenocarcinoma was detected at the site of the end-to-end anastomosis of the previous atresia.

1例胡尔勒综合征患者的先天性脐疝穿孔

对胡尔勒综合征患者的先天性脐疝(黏多糖贮积症I型),一般都采取保守治疗,因为像箝闭等并发症是很少见的,同时外科修补术的危险性很高。