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Diffuse infiltrative hemangioma of pancreas accompanied by Kasabach-Merritt Syndrome: A case report 被引量:1
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作者 Wen-Hua Zhang fang-qiong luo Hui Wang 《Chinese Medical Journal》 SCIE CAS CSCD 2020年第18期2263-2265,共3页
To the Editor:Kasabach-Merritt syndrome(KMS)is a very rare life-threatening aggressive vascular tumor that is related to Kaposiform hemangioendothelioma and tufted angioma.It is characterized by thrombocytopenia and i... To the Editor:Kasabach-Merritt syndrome(KMS)is a very rare life-threatening aggressive vascular tumor that is related to Kaposiform hemangioendothelioma and tufted angioma.It is characterized by thrombocytopenia and intravascular coagulation that occasionally develops into disseminated intravascular coagulation.[1,2]A rare incidence of diffuse infiltrative pancreatic hemangioma with a high possibility of missed diagnosis of KMS makes it a fatal disease.Here,we described a case diagnosed with diffuse infiltrative hemangioma(DIH)of pancreas accompanied by KMS and provided ultrasonic data for early and accurate diagnosis,and successful treatment experiences with sirolimus. 展开更多
关键词 diagnosis PANCREAS HEMANGIOMA
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