Osteogenesis Imperfecta is a rare genetic disorder of connective tissue that is caused by an error in collagen formation. The disease is characterized by abnormal bone fragility, osteopenia, blue discoloration of the ...Osteogenesis Imperfecta is a rare genetic disorder of connective tissue that is caused by an error in collagen formation. The disease is characterized by abnormal bone fragility, osteopenia, blue discoloration of the sclerae and hearing loss. Chronic non-suppurative otitis media is frequent in Osteogenesis Imperfecta patients and usually attributed to Eustachian tube dysfunction due to cranial molding and deformities. In some cases of severe Osteogenesis Imperfecta, the fragile bone of the petrous carotid canal can be broken down by the pulsations of the carotid artery, this may result in prolapse of the carotid artery into the protympanum with resultant Eustachian tube obstruction and tympanic membrane retraction with adhesion to prolapsed carotid artery, a condition called myringocarotidopexy.展开更多
Osteoma of the temporal bone is a rare and slow-growing benign tumor. It is reported to affect almost all portions of the temporal bone. However, osteoma involving the stylomastoid foramen has never been reported in t...Osteoma of the temporal bone is a rare and slow-growing benign tumor. It is reported to affect almost all portions of the temporal bone. However, osteoma involving the stylomastoid foramen has never been reported in the literature. We report a case of an osteoma extending from the stylomastoid foramen and occluding the external auditory canal in a young female. Although the osteoma has very close relationship with the facial nerve, it was removed because of the severity of its associated symptomatology;the osteoma was completely removed without any postoperative complications. This report is of interest as it highlights the challenges in the management of osteomas in such localization.展开更多
文摘Osteogenesis Imperfecta is a rare genetic disorder of connective tissue that is caused by an error in collagen formation. The disease is characterized by abnormal bone fragility, osteopenia, blue discoloration of the sclerae and hearing loss. Chronic non-suppurative otitis media is frequent in Osteogenesis Imperfecta patients and usually attributed to Eustachian tube dysfunction due to cranial molding and deformities. In some cases of severe Osteogenesis Imperfecta, the fragile bone of the petrous carotid canal can be broken down by the pulsations of the carotid artery, this may result in prolapse of the carotid artery into the protympanum with resultant Eustachian tube obstruction and tympanic membrane retraction with adhesion to prolapsed carotid artery, a condition called myringocarotidopexy.
文摘Osteoma of the temporal bone is a rare and slow-growing benign tumor. It is reported to affect almost all portions of the temporal bone. However, osteoma involving the stylomastoid foramen has never been reported in the literature. We report a case of an osteoma extending from the stylomastoid foramen and occluding the external auditory canal in a young female. Although the osteoma has very close relationship with the facial nerve, it was removed because of the severity of its associated symptomatology;the osteoma was completely removed without any postoperative complications. This report is of interest as it highlights the challenges in the management of osteomas in such localization.